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Hematology
Disease
Classification


Michael
Fu


• RED
BLOOD
CELL
DISORDERS

o Anemia

 Microcytic

• Iron
deficiency

• Anemia
of
chronic
disease

• Thalassemia

• Sideroblastic
anemia

 Macrocytic

• Folate
deficiency

• B12
deficiency

o Pernicious
anemia

 Normocytic,
Reticulocyte
<
3%

• Acute
blood
loss

• Aplastic
anemia

• Early
iron
deficiency

• Early
anemia
of
chronic
disease

• Chronic
renal
failure

• Malignancy

 Normocytic,
Reticulocyte
>
3%

• Non‐immune
hemolytic
anemia

o Hereditary
spherocytosis

o Hereditary
elliptocytosis

o Paroxysmal
nocturnal
hemoglobinuria

o Sickle
cell

o G6PD
deficiency

o Pyruvate

kinase
deficiency

o Acute
blood
loss

o Micro‐
and
macroangiopathic
hemolytic
anemia

o Malaria

• Autoimmune
hemolytic
anemia

o WAIHA

o CAIHA

• MYELOID
LEUKEMIA

o Chronic
myeloproliferative
disorders

 CML

 Polycythemia
vera

 Myelofibrosis
and
myeloid
metaplasia

 Essential
thrombocythemia

o Myelodysplastic
syndromes

 Refractory
anemia

 Refractory
anemia
with
ringed
sideroblasts

 Refractory
anemia
with
excess
blasts
in
transformation

 Chronic
myelomonocytic
leukemia

o AML

• LYMPHOID
LEUKEMIA

o ALL

o CLL

o Adult
T‐cell
leukemia

o Hairy
cell
leukemia

• LYMPHOMA

o Hodgkin’s
lymphoma

 Nodular
sclerosing

 Lymphocyte
dominant

 Mixed
cellularity

 Lymphocyte
depletion

o Non‐Hodgkin’s
lymphoma

 B‐cell
lymphoma

• Burkitt’s
lymphoma

• Diffuse
large
B‐cell
lymphoma

• Extranodal
marginal
zone
lymphoma

• Follicular
lymphoma

• Small
lymphocytic
lymphoma

 T‐cell
lymphoma

• Precursor
T‐cell
lymphoblastic
lymphoma

• Precursor
T‐cell
lymphoblastic
leukemia

• Mycosis
fungoides/Sezary
syndrome

o Langerhans
cell
histiocytoses

 Letterer‐Siwe
disease

 Hand‐Schuller‐Christian
disease

 Eosinophilic
granuloma

o Mast
cell
disorders

 Urticaria
pigmentosum

o Plasma
cell
dyscrasia

 Multiple
myeloma

 Monoclonal
gammopathy
of
undetermined
significance

 Solitary
skeletal
plasmacytoma

 Extramedullary
plasmacytoma

 Lymphoplasmacytic
lymphoma
(Waldenstrom’s
macroglobulinemia)

 Heavy‐chain
diseases

• HEMOSTASIS
DISORDERS

o Thrombocytopenia

 Acute
idiopathic
thrombocytopenic
purpura
(ITP)

 Chronic
idiopathic
thrombocytopenic
purpura
(ITP)

 Neonatal
alloimmune
thrombocytopenia

 Post‐transfusion
purpura

 Heparin‐induced
thrombocytopenia

 Thrombotic
thrombocytopenic
purpura
(TTP)

 Hemolytic
uremic
syndrome
(HUS)

o Thrombocytosis

 Primary

• Essential
thrombocythemia,
polycythemia
vera

 Secondary

• Chronic
iron
deficiency,
infection,
malignancy,
splenectomy

o Coagulation
disorders

 Hemophilia
A

 Hemophilia
B

 Classic
von
Willebrand
disease

 Circulating
anticoagulants

 Vitamin
K
deficiency

 Hemostasis
disorders
in
liver
disease

 Disseminated
intravascular
coagulation
(DIC)

o Fibrinolytic
disorders

 Open
heart
surgery

 Prostatectomy

 Diffuse
liver
disease

o Thrombosis
syndromes

 Acquired
thrombosis
syndromes

• Antiphospholipid
syndrome

• Malignancy

• Folate
or
B12
deficiency

• Oral
contraceptive
pill

 Hereditary
thrombosis
syndromes

• Factor
V
Leiden

• Antithrombin
III
deficiency

• Protein
C
and
S
deficiency


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